连接组织抵抗疾病 ILD

Overview

连接 tissue disease associated with interstitial lung disease, 或CT-ILD, is a lung condition that affects a small number of patients with a connective tissue disease. Examples of connective tissue diseases — also known as rheumatologic, 胶原血管或自身免疫性疾病-包括硬皮病, 类风湿性关节炎, 干燥综合征, systemic lupus erythematosus, polymyositis, dermatomyositis 和 mixed connective tissue disease.

病人 are often diagnosed with the connective tissue disease first 和 develop CT-ILD later, 尽管在某些情况下, 结果正好相反.

CT-ILD causes inflammation or scarring (fibrosis) of the lungs, or both. 肺损伤的确切原因尚不清楚.

我们对结缔组织病相关ILD的治疗方法

UCSF offers specialized care for all types of interstitial lung disease (ILD), 包括结缔组织疾病相关的ILD. 治疗包括药物治疗, care for other health problems that often affect patients with ILD, 和 a special exercise 和 education program designed for patients with chronic lung disease. Our specialists review each case as a team to ensure that every patient gets the right diagnosis 和 most effective care.

For patients who get worse despite treatment, 肺移植可能是一种选择. UCSF is home to a high-performing lung transplant program with the expertise to h和le the most complex, 具有挑战性的情况下.

奖 & 识别

是全国顶尖的十大赌博平台排行榜之一
No. 肺病学全国排名第八 & 肺部手术

迹象 & 症状

有些CT-ILD患者没有症状. 对于其他人，常见症状包括:

气短活动时呼吸短促
咳嗽
乏力
"Crackle" sound heard when listening to the chest with a stethoscope
结缔组织疾病的症状, 如关节疼痛和肿胀, 皮疹, 眼睛干涩, 口干和胃酸倒流

诊断

The diagnosis of CT-ILD requires input from pulmonologists, 放射科十大赌博平台排行榜, 在某些情况下, 病理学家对间质性肺疾病经验丰富.

在进行诊断时, your doctor will start by conducting a thorough medical history 和 physical examination. 这将包括讨论你的健康史, reviewing medications 和 potential occupational 和 environmental exposures, listening to your chest with a stethoscope to check for a crackling sound, 仔细检查你的皮肤和关节.

此外，您的十大赌博平台排行榜可能会进行以下测试:

肺功能检查. 这测试 involves a series of breathing maneuvers that measure the lungs' airflows, 你肺里的空气量, 和 the ability of your lungs to extract oxygen from the air. 这 allows your doctor to objectively assess your lung function.
高分辨率计算机断层扫描(HRCT). 这是一种特殊的 CT扫描它提供了你肺部的高分辨率图像. Images are taken in several different positions: with you lying on your back, 躺在你的胸前, 当你呼气的时候. These various images are extremely valuable in determining whether or not you have CT-ILD. Having an HRCT will feel no different than having a regular CT扫描. The 测试 is performed on an open-air table 和 takes only a few minutes.
血液测试. 血液测试 for the presence of various antibodies are used to evaluate patients for a connective tissue disease. Some patients with connective tissue diseases develop lung problems before the more typical 症状 arise; in these cases, 血液检查结果可能是CT-ILD的唯一证据.

对一些病人来说, interstitial lung disease is the first manifestation of a connective tissue disease. If this is the case, we may refer you to a rheumatologist for further evaluation.

治疗

CT-ILD is treated with anti-inflammatory or immunosuppressive medications. You may recognize some or all of these medications if they were prescribed to you for your connective tissue disease.

治疗CT-ILD最常用的药物有:

皮质类固醇(强的松)
环磷酰胺 (环磷酰胺)
霉酚酸骁悉(骁悉)

肺康复 is another important 和 effective treatment for patients with CT-ILD. 肺康复 is an exercise 和 education program designed for patients with chronic lung disease.

It's also important to pay close attention to any associated medical problems, such as 胃食管反流病(GERD) 和肺动脉高压.

For patients with worsening 症状 that don't respond to medication, 肺移植可能是一种选择.

加州大学旧金山分校健康 medical specialists have reviewed this information. It is for educational purposes only 和 is not intended to replace the advice of your doctor or other health care provider. We encourage you to discuss any questions or concerns you may have with your provider.